WebIntroduction. von Hippel–Lindau (VHL) disease is an autosomal dominant disorder that is characterized by multisystem predilection to develop tumors and cysts. 1–3 The most common tumors manifested include retinal and central nervous system hemangioblastomas, renal cell carcinoma, pheochromocytoma, and pancreatic … A pheochromocytoma (fee-o-kroe-moe-sy-TOE-muh) is a rare, usually noncancerous (benign) tumor that develops in an adrenal gland. You have two adrenal glands — one located at the top of each kidney. The adrenal glands are part of the body's hormone-producing (endocrine) system. The endocrine system also … See more Signs and symptoms of pheochromocytomas often include: 1. High blood pressure 2. Headache 3. Heavy sweating 4. Rapid … See more Researchers don't know exactly what causes a pheochromocytoma. The tumor develops in specialized cells, called chromaffin cells, located in the center of an adrenal gland. These cells release certain hormones, … See more High blood pressure can damage organs, particularly tissues of the heart and blood vessel (cardiovascular) system, brain and kidneys. This damage … See more Most pheochromocytomas are discovered in people between the ages of 20 and 50. But the tumor can develop at any age. People who have … See more
Pheochromocytoma: Causes, Symptoms & Treatment
WebIntroduction. von Hippel–Lindau (VHL) disease is an autosomal dominant disorder that is characterized by multisystem predilection to develop tumors and cysts. 1–3 The most … WebThis type of tumor can occur in certain familial genetic syndromes, including multiple endocrine neoplasia, type 2 (MEN2), neurofibromatosis type 1, Von Hippel-Lindau disease, … myn investments llc
Pheochromocytoma - StatPearls - NCBI Bookshelf
WebOct 3, 2024 · Sporadic pheochromocytoma is usually diagnosed on the basis of symptoms or an incidental discovery on computed imaging, whereas syndromic pheochromocytoma is frequently diagnosed earlier in the course of disease because of biochemical surveillance or genetic testing. (See "Pheochromocytoma in genetic disorders" .) WebFeb 12, 2024 · Pheochromocytoma is a rare neuroendocrine tumor, occurring in less than 0.2 percent of patients with hypertension [ 1,2 ]. In approximately 60 percent of patients, the tumor is discovered incidentally during computed tomography (CT) or magnetic resonance imaging (MRI) of the abdomen for unrelated symptoms [ 3 ]. WebNov 26, 2024 · Only 1 patient with a T1 SDHB (+) pheochromocytoma had stage IV disease with metastasis to the liver and the skeleton. The majority of patients (59.2%) had T2 … myn investments